ENDOCRINE SOCIETY

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Hyperandrogenism-induced Athletic Excellence in a Young Patient with Adrenocortical Carcinoma: 10 Years of Remission

Takashi Kono,1,2 Satomi Kono,1 Yasuhiro Nakamura,3 Yoichi Fujii,4 Hironobu Sasano, 1,5 and Tomoaki Tanaka 1,2 iD

1Department of Molecular Diagnosis, Chiba University Graduate School of Medicine, Chiba 260-8670, Japan

2Research Institute of Disaster Medicine, Chiba University, Chiba 260-8670, Japan

3Division of Pathology, Faculty of Medicine, Tohoku Medical and Pharmaceutical University, Miyagi 983-8536, Japan

4Department of Pathology and Tumor Biology, Graduate School of Medicine, Kyoto University, Kyoto 606-8501, Japan 5Department of Pathology, Tohoku University School of Medicine, Sendai, Miyagi 980-8575, Japan

Correspondence: Tomoaki Tanaka, MD, PHD, Department of Molecular Diagnosis, Chiba University Graduate School of Medicine, 1-8-1 Inohana, Chuo-ku, Chiba 260-8670, Japan. Email: tomoaki@restaff.chiba-u.jp.

Abstract

A 17-year-old female softball player presented with progressive virilization and markedly enhanced athletic performance. Laboratory evaluation revealed elevated serum testosterone with autonomous adrenal secretion. Imaging analysis demonstrated an 8-cm right adrenal mass. Adrenalectomy was performed, and histopathological examination confirmed stage Il adrenocortical carcinoma (ACC) with a Ki-67 labeling index of 14%. Postoperatively, she received adjuvant mitotane therapy. At 34 months, a solitary hepatic metastasis was successfully treated with radiofrequency ablation and combination chemotherapy. She has remained disease-free for more than 8 years following initial surgery. This case demonstrates the clinical impact of pathological hyperandrogenism on athletic performance and highlights the potential for long- term remission in young patients with aggressive ACC managed through multimodal therapy.

Key Words: adrenocortical carcinoma, hyperandrogenism, athletics, androgen, virilization

Introduction

Adrenocortical carcinoma (ACC) is a rare endocrine malig- nancy with an incidence of 1 to 2 cases per million [1]. Hormonal excess is the predominant presenting feature, with approximately 20% exhibiting isolated androgen excess and 22% combined cortisol-androgen secretion [2]. Androgen ex- cess in females typically manifests as virilization-hirsutism, voice deepening, and menstrual irregularities.

Excess androgens enhance skeletal-muscle development and athletic performance through multiple mechanisms: in- creased protein synthesis, preferential type II muscle fiber de- velopment, and improved neuromuscular adaptation [3], resulting in measurable performance gains [4]. While andro- genic effects have been well studied therapeutically, patho- logical hyperandrogenism from endocrine malignancies remains poorly understood in sports medicine, particularly during adolescence [5].

This report describes ACC-induced hyperandrogenism in a 17-year-old athlete, quantifying exceptional performance gains through standardized assessments and highlighting the anabolic impact of pathological androgens.

Case Presentation

A 17-year-old female varsity softball player presented with a 2-year history of progressive hirsutism, amenorrhea, and

voice deepening. Following a national training program, her performance metrics (grip strength, sprint time) exceeded age- matched norms by >2 SD. Her performance gains exceeded her teammates, without exogenous steroid use.

Menarche occurred at age 12 with regular cycles until age 15, when oligomenorrhea developed alongside worsening hir- sutism. Physical examination findings are shown in Fig. 1A.

Physical fitness assessments (T-scores: mean 50, SD 10) re- vealed improvements from ages 13 to 17, particularly grip strength (T 56.8 109.3), nearly doubling Japanese female norms [6]. Similar gains occurred in cardiorespiratory endurance [7], power output, and muscular strength (Table 1, Fig. 1B).

Physical examination revealed height 165.7 cm, weight 62.4 kg, body mass index 22.7 kg/m2, and blood pressure 130/70 mmHg. Virilization signs included hirsutism (Ferriman- Gallwey score 14; normal <8), acne, clitoromegaly (1 cm), and increased muscle mass without cushingoid features.

Diagnostic Assessment

Endocrine evaluation revealed androgen elevation (Table 2): testosterone 65.2 ng/ml (226 nmol/L) [reference 0.11-0.47 ng/ml (0.38-1.63 nmol/L)], dehydroepiandrosterone sulfate (DHEA-S) 1970µg/dL (53.8 umol/L) [reference 51-321 µg/dL (1.39-8.76 umol/L)], and androstenedione 55 ng/ml (192 nmol/L) [reference 0.11-0.39 ng/ml (0.38-1.36 nmol/L)]. High-dose

Figure 1. Clinical presentation and athletic performance enhancement. (A) Preoperative photographs showing virilization signs with increased muscle mass and male-pattern body habitus. (B) Radar chart comparing standardized physical fitness measurements (T-scores) at ages 13 (solid blue line) and 17 years (solid red line) relative to age-matched national norms (solid gray reference line, T= 50). Marked improvements in grip strength, sprint speed, and other performance metrics correlate with the period of pathological hyperandrogenism.

A

B

Grip.Strength

Age 13

100

Age 17

National Average (T = 50)

Sit.ups

80

Softball.Throw

60

40

20

Sitting- TrunkFlexion

Standing. Longjump

Side.Steps

50m.Sprint

20m.Shuttle.Run

Table 1. Physical fitness test results and T-scores in a female patient with androgen-producing adrenocortical carcinoma from ages 13 to 17 years
ParameterAge 13Age 16Age 17
RawT-scoreRawT-scoreRawT-score
Muscle function56.846 kg109.3
Grip strength27 kg88.057 kg
Power output
Standing long jump175 cm52.3200 cm62.3225 cm71.7
Softball throw18 m49.725 m73.225 m73.2
Speed
50 m sprint8.5 second53.77.29 second67.26.88 second71.1
Endurance
20 m shuttle run73 counts56.7101 counts73.9116 counts79.7
Sit-ups27 counts56.928 counts57.835 counts67.0
Trunk mobility
Sitting trunk flexion43 cm49.142 cm45.554 cm56.0
Side steps47 counts52.250 counts50.655 counts52.4

T-score = 50 + 10 x [(raw value - population mean)/population SD]. T-scores are standardized to a population mean of 50 and SD of 10 for age- and sex-matched Japanese adolescents. Normative values were derived from the National Physical Fitness Survey (2008-2012; n = 12 405 females) conducted by the Japan Sports Agency. Adrenocortical carcinoma diagnosed at age 17.

dexamethasone suppression testing demonstrated inadequate cortisol suppression (9.4 µg/dL (259 nmol/L) after 8 mg [nor- mal <1.8 µg/dL (<50 nmol/L)] with a paradoxical increase in testosterone, confirming autonomous hormone production.

Computed tomography (CT) revealed an 8-cm heterogeneous right adrenal mass with contrast enhancement (Fig. 2A), with- out metastases. Endocrine and imaging findings established the diagnosis of androgen-producing ACC with subclinical Cushing syndrome.

Treatment

The patient underwent laparoscopic adrenalectomy at age 17. R0-resection was achieved, with an intact capsule and nega- tive margins, and discharge was on postoperative day 3.

Pathology revealed a 13.5x 8.5 × 8.3 cm tumor weighing 119 g with high-grade nuclear atypia, >5 mitoses per 50 high- power fields and Ki-67 14%. Six of 9 Weiss criteria-high nuclear grade, elevated mitotic rate, atypical mitoses, eosinophilic cytoplasm, diffuse architecture, and capsular

Table 2. Baseline hormonal assessment and loading test results
ParameterValue (SI units)Reference range (SI units)
ACTH-08:007.7 pg/mL (1.7 pmol/L)7.2-63.3 pg/mL (1.6-13.9 pmol/L)
ACTH-20:00<5.0 pg/mL (<1.1 pmol/L)<10 pg/mL (<2.2 pmol/L)
Cortisol-08:007.0 µg/dL (193 nmol/L)6.2-19.4 µg/dL (171-535 nmol/L)
Cortisol-24:004.0 µg/dL (110 nmol/L)<10 µg/dL (<276 nmol/L)
DHEA-S1970 µg/dL (53.8 µmol/L)51-321 µg/dL (1.39-8.76 µmol/L)
E272 pg/mL (264 pmol/L)30-400 pg/mL (110-1468 pmol/L)
Testosterone65.2 ng/ml (226 nmol/L)0.11-0.47 ng/ml (0.38-1.63 nmol/L)
Androstenedione55 ng/ml (192 nmol/L)0.11-0.39 ng/ml (0.38-1.36 nmol/L)
TSH0.903 µIU/mL (0.903 mIU/L)0.4-4.5 uIU/mL (0.4-4.5 mIU/L)
FT32.59 pg/mL (3.98 pmol/L)2.3-4.2 pg/mL (3.5-6.5 pmol/L)
FT40.99 ng/dL (12.7 pmol/L)0.8-1.8 ng/dL (10.3-23.2 pmol/L)
LH0.05 mIU/mL (0.05 IU/L)0.5-7.63 mIU/mL (0.5-7.63 IU/L)
FSH0.06 mIU/mL (0.06 IU/L)1.5-3.34 mIU/mL (1.5-3.34 IU/L)
Urine cortisol (24 hours)86.6 µg/day10-100 µg/day
(239 nmol/day)(27.6-276 nmol/day)
ParameterBaseline (SI units)After 2 mg (SI units)After 8 mg (SI units)Reference range (SI units)
ACTH7.7 pg/mL (1.7 pmol/L)<1.0 pg/mL (<0.22 pmol/L)<1.0 pg/mL (<0.22 pmol/L)7.2-63.3 pg/mL (1.6-13.9 pmol/L)
Cortisol7.0 µg/dL (193 nmol/L)8.6 µg/dL (237 nmol/L)9.4 µg/dL (259 nmol/L)< 1.8 µg/dL (< 50 nmol/L)
Androstenedione55 ng/ml (192 nmol/L)ND87 ng/ml (304 nmol/L)0.11-0.39 ng/ml (0.38-1.36 nmol/L)
DHEA-S1970 µg/dL (53.8 µmol/L)ND2640 µg/dL (71.9 µmol/L)51-321 µg/dL (1.39-8.76 µmol/L)
Testosterone65.2 ng/ml (226 nmol/L)94.7 ng/ml (328 nmol/L)92.9 ng/ml (322 nmol/L)0.11-0.47 ng/ml (0.38-1.63 nmol/L)

Dexamethasone suppression test results

Abbreviations: DHEA-S, dehydroepiandrosterone sulfate; E2, estradiol; ND, not detected; FT3, free T3; FT4, free T4.

invasion-established high-grade ACC (Fig. 2C and 2D). The final stage was T2N0M0 (stage II).

Postoperatively, mitotane was escalated from 1.5 to 4.5 g/ day over 3 weeks, maintaining plasma 14 to 20 mg/L by regu- lar monitoring [8]. Hydrocortisone 40 mg daily prevented ad- renal insufficiency, and this regimen accords with current guidelines for high-risk ACC [9-12].

Outcome and Follow-up

Following confirmation of high-grade ACC (stage II; Ki-67 14%), we performed molecular and immunohistochemical studies to elucidate the extreme androgen excess.

Comprehensive immunohistochemistry of the resected tu- mor demonstrated intense staining for CYP17A1 and cyto- chrome b5, indicating 17,20-lyase activity that preferentially channels precursors toward androgen synthesis. HSD3B2

was likewise strongly positive, whereas CYP21A2 showed only a weak to moderate signal, explaining relatively pre- served cortisol production despite massive androgen output. StAR and CYP11B1 were moderately expressed; SULT2A1 was minimal, confirming selective androgen hypersecretion (Fig. 2E-2K).

Whole-exome sequencing identified somatic BCOR-P1384R and HDAC9-R947P mutations, reported in <3% of ACCs and predicted pathogenic by in silico analysis [13, 14]. TP53 and CTNNB1, the most common drivers in adult ACC, were wild-type. Genome-wide copy-number profiling revealed the gains and losses typical of ACC (Fig. 3) [15-17], fitting a rare BCOR/HDAC9-mutant subset of the recog- nized spectrum.

Postoperative follow-up consisted of quarterly endocrine testing and alternating CT/magnetic resonance imaging every 6 months. At 34 months, a 4-mm segment VIII liver nodule

Figure 2. Radiological, pathological, and immunohistochemical characteristics of the virilizing adrenocortical carcinoma. (A) Contrast-enhanced computed tomography showing a large heterogeneous mass in the right adrenal gland with areas of necrosis and hemorrhage. (B) Gross appearance of the resected tumor demonstrating a reddish-brown, well-encapsulated mass with areas of hemorrhage and necrosis. (C) Hematoxylin and eosin staining showing typical adrenocortical carcinoma morphology with sheets of polygonal cells, nuclear pleomorphism, and increased mitotic activity (x200 magnification). (D) Ki-67 immunostaining revealing high proliferative activity with scattered positive nuclei (x400 magnification). (E) StAR protein immunostaining showing moder- ate cytoplasmic positivity (++), confirming steroidogenic capacity (x400 magnification). (F) CYP21A2 (21ß-hydroxylase) immunostaining demonstrating weak to moderate positivity (+/++), consistent with relatively suppressed cortisol biosynthesis (x400 magnification). (G) Cytochrome b5 immunostaining showing intense diffuse positivity (+++), indicating enhanced 17,20-lyase activity promoting androgen production (x400 magnification). (H) CYP17A1 (17a-hydroxylase/17,20-lyase) immunostaining revealing strong diffuse positivity (+++), explaining the robust androgen biosynthetic capacity (x400 mag- nification). (I) HSD3B2 (3ß-hydroxysteroid dehydrogenase) immunostaining showing strong positivity (+++), confirming active steroidogenesis (x400 mag- nification). (J) CYP11B1 (11ß-hydroxylase) immunostaining demonstrating moderate positivity (++), indicating preserved late-stage cortisol biosynthetic capacity (x400 magnification). (K) SULT2A1 (sulfotransferase 2A1) immunostaining showing minimal expression (±), suggesting that elevated dehydroe- piandrosterone sulfate levels were due to substrate excess rather than enhanced enzyme activity (x400 magnification). The immunohistochemical profile explains the selective androgen hypersecretion: strong CYP17A1 and cytochrome b5 expression drives preferential 17,20-lyase activity, while relatively weak CYP21A2 expression limits cortisol production, collectively resulting in extreme testosterone elevation (139-fold above normal) with maintained cor- tisol levels. Scale bars represent 50 um in all panels.

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50 um

50 pm

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Figure 3. Genomic characterization of the tumor. Copy number variation profile demonstrating characteristic chromosomal alterations, including amplifi- cations (solid red box, amp.) in chromosomes 1q, 2p, and 5p and deletions (solid blue box, del.) in chromosomes 3, 11, and 22, consistent with the genomic landscape typically observed in adrenocortical carcinoma.

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Figure 4. Liver metastasis during follow-up. (A) MRI image at 34 months postsurgery showing a small liver metastasis (white arrowheads). (B) Follow-up MRI at 38 months showing enlargement of the lesion prior to intervention with radiofrequency ablation and combination chemotherapy (white arrowheads). Abbreviation: MRI, magnetic resonance imaging.

emerged and enlarged to 12 mm over 4 months (Fig. 4A and 4B). In view of the small size, subcapsular location, and high Ki-67 index of the primary tumor, percutaneous radiofre- quency ablation (RFA) was selected instead of hepatic resec- tion [18]. Mitotane, previously tapered to maintenance, was re-escalated (1.0 1.5 g/day) and combined with 3 cycles of etoposide, doxorubicin, and cisplatin. Hydrocortisone and flu- drocortisone were titrated.

RFA achieved complete local control, and subsequent im- aging has shown no recurrence for more than 8 years. Mitotane was discontinued after 2 consecutive years of nega- tive scans while low-dose hydrocortisone (20 mg) was contin- ued. Serum testosterone, DHEA-S, and androstenedione remain within reference limits (Fig. 5A).

Serial cross-sectional imaging at the L3 vertebral level quantified the reversal of androgen-driven hypertrophy [19]. Preoperative skeletal-muscle area and skeletal-muscle index (SMI) were 150.2 cm2 and 55.8 cm2/m2, respectively- well above female norms. Skeletal-muscle area/SMI fell to 120.1 cm2 and 44.2 cm2/m2 at 6 months, 95.2/35.0 cm2/m2 at 20 months, and 62.5/23.0 cm2/m2 at 45 months, represent- ing an overall 59% decline. The final SMI lies below consensus

sarcopenia thresholds for both sexes, corroborating the patient’s subjective loss of explosive strength during daily activity. (Fig. 5B and 5C).

The patient’s menstrual cycles resumed 14 months after mi- totane withdrawal and stabilized at 30- to 45-day intervals, indicating partial recovery of hypothalamic-pituitary-ovarian function. Formal postoperative athletic testing was not per- formed, but the patient noted greater fatigue in sprinting and throwing activities than during endurance exercise, con- sistent with the preferential androgen effect on fast-twitch type II fibers. Her body composition normalized with re- duced shoulder and upper-arm definition and increased ilio- femoral adiposity.

Co-expression of CYP17A1 and cytochrome b5 is crucial: cytochrome b5 enhances the 17,20-lyase reaction, diverting pregnenolone and progesterone toward androgen synthesis. This cooperative mechanism, documented in fewer than 10% of ACCs, explains the tumor’s testosterone output. Weak CYP21A2 further restrains cortisol biogenesis, preventing ad- renal insufficiency while permitting androgen precursors to ac- cumulate. Minimal SULT2A1 hampers sulfation and clearance of DHEA. This biochemical milieu yielded a serum DHEA-S of

Figure 5. Comprehensive treatment course, hormonal profile, and body composition changes over 132 months. (A) Timeline showing therapeutic interven- tions and hormonal measurements during follow-up. Upper section displays hydrocortisone (light green), dexamethasone (dark green), and mitotane (orange) dosing. Lower section shows serum levels of dehydroepiandrosterone sulfate (purple), testosterone (blue), and cortisol (green, F). Black arrowheads indicate timing of surgery; radiofrequency ablation; and etoposide, doxorubicin, cisplatin, and mitotane chemotherapy. Note the rapid normalization of androgen levels following tumor resection and sustained normal levels throughout the follow-up period. (B) Progressive decline in skeletal muscle area (circles) and skeletal muscle index (squares) over 45 months following surgical resection. Both parameters show continuous reduction from pathologically elevated preoperative values to sarcopenic levels. (C) Representative axial computed tomography images at the L3 vertebral level demonstrating marked reduction in skeletal muscle mass over time. Upper row (left to right): preoperative, 3 months, 6 months postoperative. Lower row (left to right): 12 months, 20 months, 32 months post- operative. Note the progressive decrease in muscle area and increased intramuscular fat infiltration.

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3 months post op

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1970 µg/dL, among the highest in adolescent ACC, underscor- ing the diagnostic value of enzyme-level mapping.

This case illustrates that aggressive multimodal treatment- R0 adrenalectomy, sustained mitotane exposure, and definitive

therapy for oligometastatic relapse-can deliver durable remis- sion in high-risk adolescent ACC. Integration of immunohisto- chemical, genomic, and functional readouts clarified tumor biology; guided surveillance intensity; and provided objective

documentation of the reversible anabolic impact of pathologic- al hyperandrogenism. Ongoing management focuses on life- long endocrine follow-up; bone-mineral monitoring; and counseling regarding fertility, pregnancy, and adrenal-crisis prevention. At the latest review-9 years after the initial operation-the patient remains recurrence-free, normotensive, and engaged in full-time study.

Discussion

We report ACC-driven hyperandrogenism in a 17-year-old softball player achieving remission through surgery, mitotane, RFA, and chemotherapy. Key findings include (1) marked fiber-type-specific athletic performance gains from pathological androgens, (2) rare BCOR/HDAC9 mutations expanding the molecular spectrum of ACC, and (3) aggressive treatment and long-term management yielding >8-year disease-free survival.

Supraphysiologic testosterone produced gains most evident in power tasks relying on fast-twitch (type II) fibers: grip strength almost doubled, and standing long-jump rose 46%. Endurance capacity, dependent on type I fibers, increased 26%. This differential mirrors laboratory work showing that androgens preferentially expand type II myofibers and in- crease motor-unit firing [20, 21], while oxidative capacity ris- es modestly. While a causal relationship is likely, underlying genetic or training-related factors may have contributed to the observed gains. In competitive sports, performance gains exceeding 2 SDs above population norms may trigger anti-doping investigations. Therefore, clinicians and regula- tory authorities should consider underlying endocrine disor- ders, including rare tumors like ACC, to prevent diagnostic errors and avoid unjust sanctions [22].

Immunohistochemistry confirmed a steroidogenic profile di- verting precursors toward testosterone: intense CYP17A1 + cytochrome b5, weak-moderate CYP21A2, strong HSD3B2, and minimal SULT2A1.

To better understand the molecular drivers of the tumor’s aggressive and hyperandrogenic phenotype, we performed whole-exome sequencing, which uncovered 2 rare somatic mutations-BCOR P1384R and HDAC9 R947P-in the ab- sence of TP53 or CTNNB1 alterations. Each variant occurs in <3% of catalogued ACCs and is predicted pathogenic, ex- panding the spectrum of epigenetic regulators implicated in pediatric ACC. While the prognostic significance of these BCOR/HDAC9 variants remains uncertain, their identifica- tion highlights the molecular heterogeneity of ACC beyond common TP53/CTNNB1 alterations.

Although laparoscopic resection of tumors >6 cm remains controversial, we achieved R0 margins despite the 8-cm size, as imaging showed a well-encapsulated lesion without vascular invasion, our center had extensive laparoscopic experience, and the patient preferred a minimally invasive approach. Current guidelines for ACC management emphasize the importance of complete surgical resection and adjuvant therapy in high-risk cases [23]. Mitotane was titrated to 14 to 20 mg/L, and quarter- ly laboratory review plus semi-annual CT/magnetic resonance imaging provided surveillance. At 34 months, a segment VIII liver nodule emerged (4 mm) and grew to 12 mm within 4 months. Given its subcapsular location, percutaneous RFA was chosen [18]; mitotane was re-escalated and 3 cycles of eto- poside, doxorubicin, and cisplatin added. This strategy achieved complete remission exceeding 8 years, far surpassing

the ~35% 5-year survival typical of stage II ACC. Long-term follow-up has focused on managing adrenal insufficiency, mon- itoring anthracycline cardiotoxicity risk, and addressing skeletal-muscle loss following androgen normalization.

Serial L3 CT images showed an SMI decline from 55.8 to 23.0 cm2/m2 (-59%) over 45 months-below the 29 cm2/m2 threshold for young women-mirroring loss of explosive power. Menstruation resumed 14 months after mitotane cessa- tion, and body composition shifted toward a typical female pat- tern, highlighting the reversible-but quality-of-life-relevant- impact of pathological androgen excess. Given the substantial quality-of-life impact of androgen withdrawal and treatment sequelae, survivorship planning for young women with ACC must also include fertility preservation, psychosocial support, and adrenal-crisis preparedness.

Durable remission also demands structured toxicity monitoring. Mitotane can impair cognition and raise lipids, while cumulative anthracycline doses threaten cardiomy- opathy. Our protocol includes annual echocardiography, lipid profiling, neurocognitive testing, dual-energy X-ray absorptiometry scans, and emergency hydrocortisone edu- cation cards.

Study limitations include uncertain prognostic significance of BCOR/HDAC9 variants and single-case design. Multicenter registries are needed to validate these findings and refine ACC risk stratification in athletes.

Learning Points

· Pathological hyperandrogenism from ACC can dramatic- ally enhance athletic performance, with reversible effects following treatment.

· Aggressive multimodal therapy (surgery, mitotane, RFA for oligometastatic disease) achieved long-term remission in this high-risk ACC (Ki-67 14%), suggesting potential benefit of comprehensive treatment in young patients.

· Exceptional athletic gains with virilization in young ath- letes warrant endocrine evaluation to exclude underlying pathologies.

· Young women with ACC require comprehensive care ad- dressing both oncological outcomes and quality-of-life is- sues, including fertility and adrenal insufficiency.

· Clinicians and sports authorities must remain vigilant for pathological hyperandrogenism, which can mimic doping and lead to misclassification in athletic contexts.

Acknowledgments

We thank Professor Seishi Ogawa at the Department of Pathology and Tumor Biology, Graduate School of Medicine, Kyoto University for genomic analysis.

Contributors

T.K. and T.T. diagnosed and managed the patient; T.T. led endocrine evaluation/planning; T.K., S.K., and Y.F. per- formed molecular/genetic analyses; Y.N. and H.S. interpreted pathology; T.K. and T.T. drafted the manuscript.

Funding

None.

Disclosures

The authors have nothing to disclose.

Signed informed consent was obtained from the patient.

Data Availability Statement

Some or all datasets generated during and/or analyzed during the current study are not publicly available but are available from the corresponding author on reasonable request.

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