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Pan-cancer analysis reveals the roles of XPO1 in predicting prognosis and tumorigenesis

Lei Zhao1, Baiwei Luo2, Liang Wang3, Wei Chen1, Manyu Jiang2, Nengwei Zhang4

1Department of Critical Care Medicine, Beijing Shijitan Hospital, Capital Medical University, Beijing, China; 2The First Clinical Medical School of Guangdong Medical University, Zhanjiang, China; ‘Department of Hematology, Beijing TongRen Hospital, Capital Medical University, Beijing, China; 4Surgery Centre of Diabetes Mellitus, Beijing Shijitan Hospital, Capital Medical University, Beijing, China

Contributions: (I) Conception and design: N Zhang, L Zhao; (II) Administrative support: L Wang; (III) Provision of study materials or patients: N Zhang, L Zhao, L Wang; (IV) Collection and assembly of data: B Luo; (V) Data analysis and interpretation: B Luo; (VI) Manuscript writing: All authors; (VII) Final approval of manuscript: All authors.

Correspondence to: Nengwei Zhang, MD. Surgery Centre of Diabetes Mellitus, Beijing Shijitan Hospital, Capital Medical University, No. 10 Tieyi Rd, Haidian District, Beijing 100038, China. Email: znw@bjsjth.cn.

Background: Exportin 1 (XPO1), a nuclear export protein, participates in many biological processes, including mRNA transport, nucleocytoplasmic transport, nuclear protein export, regulation of mRNA stability, and drug response. XPO1 plays key roles in many cancer types and may serve as a potential biomarker. It is significant to systematically elucidate the roles of XPO1 in various cancer types in terms of function, molecular biology, immunology, and clinical relevance.

Methods: Data from UCSC Xena, CCLE, and CBioPortal were analyzed for the investigation of the differential expression of XPO1 across multiple cancer types. Clinical data were acquired to analyze the influence of XPO1 on the clinical characteristics of patients, such as survival outcome and clinical stage. The roles of XPO1 in the onset and progression of multiple cancers were expounded in terms of genetic changes at the molecular level [including tumor mutational burden (TMB), microsatellite instability (MSI), copy number variation (CNV), methylation, and gene co-expression], biological pathway changes, and the immune microenvironment.

Results: XPO1 was overexpressed in various tumor types, which may be related to CNV. Clinical data analysis revealed that XPO1 may serve as a risk factor in tumors, such as adrenocortical carcinoma, liver hepatocellular carcinoma, and low-grade glioma, thereby affecting patient prognosis. XPO1 in multiple tumor types was also substantially correlated with clinical stage, patient gender, and patient age. In certain tumors, the expression level of XPO1 exerted a greater influence on TMB and MSI. It was also found that XPO1 inhibited the activity of immune cells in the tumor immune microenvironment, such as CD8+ T cells, and affected biological pathways, such as the cell cycle and oxidative phosphorylation, and drove the expression of cancer driver genes, immune checkpoint genes, and highly mutated genes.

Conclusions: XPO1 is a potential pan-cancer risk factor as it may jointly promote tumor onset and progression by inhibiting the immune response, influencing relevant biological pathways, and promoting mutations in other genes.

Keywords: Exportin 1 (XPO1); pan-cancer; tumor mutational burden (TMB); microsatellite instability (MSI); immune microenvironment

Submitted Aug 15, 2021. Accepted for publication Oct 14, 2021.

doi: 10.21037/tcr-21-1646

View this article at: https://dx.doi.org/10.21037/tcr-21-1646

Introduction

The nuclear export protein Exportin 1 (XPO1) plays a key role in the onset and progression of both solid tumors and hematological malignancies and is associated with a poor prognosis in patients with various cancers, including pancreatic, lung, gastric, prostate, and colorectal cancers (1). Selective inhibitors of XPO1, with selinexor being one of the most representative drugs, have been widely tested in solid tumors and hematological malignancies and approved for the treatment of relapsed/refractory multiple myeloma and diffuse large B-cell lymphoma (2,3). Some studies have suggested that XPO1 may promote tumor cell proliferation by influencing the sub-cellular localization of nuclear export signal-containing oncogenes, tumor suppressor proteins, control of the mitotic apparatus, chromosome segregation, stability of nuclear and chromosomal structures (4). Notably, XPO1 is the major transporter of many types of nuclear proteins, including tumor suppressor proteins and oncoproteins, such as Rb, APC, p53, p21, p27, BRCA1/2, eIF4E, and survivin (1,4,5). This indicates that XPO1 plays a critical role in the progression of many tumors. Besides directly influencing the expression of proto-oncogenes and tumor suppressor genes, XPO1 can also indirectly promote tumor onset and progression by affecting vascular endothelial growth factor, epidermal growth factor receptor, Cox-2, c-Myc, and HIF-1 (5). Based on these findings, it is evident that XPO1 does not affect tumor progression by a single route but exerts biological effects on tumors through multiple pathways. Therefore, elucidating the roles of XPO1 in various tumors based on clinical-omics and genomics is essential to provide theoretical guidance for future drug development and clinical treatment.

We present the following article in accordance with the REMARK reporting checklist (available at https://dx.doi. org/10.21037/tcr-21-1646).

Methods

Data sources

The mRNA expression data, clinical data, and methylation data of 33 tumor types and normal tissues were downloaded from UCSC Xena (https://xena.ucsc.edu/). The tumor types investigated in this study included adrenocortical carcinoma (ACC), urothelial bladder carcinoma (BLCA), infiltrating ductal carcinoma (BRCA), cervical squamous cell carcinoma and endocervical adenocarcinoma (CESC), cholangiocarcinoma (CHOL), colon adenocarcinoma (COAD), diffuse large B-cell lymphoma (DLBC),

esophageal carcinoma (ESCA), glioblastoma multiforme (GBM), head and neck squamous cell carcinoma (HNSC), kidney chromophobe renal cell carcinoma (KICH), kidney clear cell renal cell carcinoma (KIRC), kidney renal papillary cell carcinoma (KIRP), acute myeloid leukemia (LAML), low-grade glioma (LGG), liver hepatocellular carcinoma (LIHC), lung adenocarcinoma (LUAD), lung squamous cell carcinoma (LUSC), mesothelioma (MESO), ovarian serous cystadenocarcinoma (OV), pancreatic adenocarcinoma (PAAD), pheochromocytoma/paraganglioma (PCPG), prostate adenocarcinoma (PRAD), rectum adenocarcinoma (READ), sarcoma (SARC), skin cutaneous melanoma (SKCM), stomach adenocarcinoma (STAD), testicular germ cell tumor (TGCT), thyroid carcinoma (THCA), thymic carcinoma (THYM), uterine corpus endometrial carcinoma (UCEC), uterine carcinosarcoma (UCS), and uveal melanoma (UVM). The mRNA expression data of various cancer cell lines were downloaded from CCLE (https://portals.broadinstitute.org/ccle), and the copy number variation (CNV) data of XPO1 in the 33 types of tumors were downloaded from CBioPortal (https://www. cbioportal.org/). All procedures performed in this study involving human participants were in accordance with the Declaration of Helsinki (as revised in 2013).

Differential expression of XPO1

To determine the differential expression of XPO1 in normal and tumor tissues, the data of XPO1 expression in the 33 tumor types downloaded from UCSC Xena were first transformed to the normalized transcripts per million format, and boxplots were plotted using the ggpubr and ggplot2 R packages (6). The statistical significance of differential XPO1 expression in the various tumors was determined using the Wilcoxon signed-rank test.

Correlations of XPO1 with clinical characteristics

To evaluate the effects of XPO1 expression on overall survival (OS), disease-specific survival (DSS), disease- free interval (DFI), and progression-free interval (PFI) in patients, tumor samples were divided into the two following groups: the high expression group and low expression group, based on the median XPO1 expression level among the various tumor types. Subsequently, survival analysis was performed using the log-rank test in the survival R package, and results were visualized using the survminer R package. A Cox proportional hazards model was also computed

in the survival R package for survival analysis, and forest plots were drawn using the forestplot R package for the visualization of analysis results. The influence of XPO1 on patient survival in various cancers was investigated using the Kaplan-Meier Plotter (https://kmplot.com/analysis/) (7).

Correlations of XPO1 with patient age (≤18 years: adolescence; 19-30 years: adulthood; 31-50 years: middle- aged; >51 years: older), sex, and clinical stage were investigated. Boxplots were drawn using the ggpubr and ggplot2 R packages (6), and the statistical significance of the potential clinical correlations was determined using the Wilcoxon signed-rank test.

Characteristics of molecular-level changes of XPO1 and their molecular effects

Data regarding the CNVs of XPO1, including amplifications and deletions, were downloaded from CBioPotal (https://www. cbioportal.org/) for the calculation of CNV frequency among the various tumor types. Correlations between CNV and XPO1 expression level were determined using the Wilcoxon signed-rank test and visualized using the ggpubr R package. The Spearman’s rank correlation coefficients for correlations of XPO1 expression with tumor mutational burden (TMB) and microsatellite instability (MSI) in the various tumors were separately calculated, and radar charts were plotted using the fmsb R package. The statistical significance of differences in XPO1 methylation level in normal and tumor tissues was determined using the Wilcoxon signed-rank test, and results were visualized using the ggplot2 R package (6). Based on the median XPO1 methylation level, tumor samples were divided into the two following groups: the high methylation group and low methylation group, and survival analysis was performed using the survival R package. Mutations of XPO1 in the 33 tumor types were recorded, and the Spearman’s rank correlation coefficients between XPO1 expression and the expression of the top 30 highly mutated genes among the various tumor types were separately calculated.

Effects of XPO1 on the immune microenvironment

To determine the effects of XPO1 on the immune microenvironment in various tumor types, the stromal and immune scores of the tumors were evaluated using the ESTIMATE algorithm (8). The Spearman’s rank correlation coefficients for correlations of XPO1 expression with the stromal scores and the immune scores were separately calculated. Relative contents of 22 types of

immune cells in the various tumor types were calculated using the CIBERSORT algorithm (9). Then the Spearman’s rank correlation coefficients between XPO1 expression and the various immune cell types were calculated.

Co-expression of XPO1 and specific genes

Co-expression analyses of XPO1 with immune-related genes and cancer driver genes were separately performed for further determination of XPO1 functions. The Pearson correlation coefficients between expression levels of XPO1 and the various immune checkpoint genes were calculated. We used the edgeR R package (10,11) to perform differential analysis between normal and tumor group. Next, we chose five genes with the highest log FC values among the 568 driver genes (12) for each tumor type, and the driver genes with the greatest difference were determined through the union of data for the various tumor types. The Pearson correlation coefficients between XPO1 expression and the driver genes with the greatest difference were calculated. Based on the median value of XPO1 expression, tumor samples were divided into the high expression group and low expression group, and differential analysis was performed using the edgeR R package (10,11). Gene set enrichment analysis (GSEA) was subsequently performed using the clusterProfiler R package (13). The top five genes with the highest absolute values for the normalized enrichment score and P<0.05 were identified for each tumor type, and the results were visualized.

Statistical analysis

All analyses were carried out in R version 3.6.1 and corresponding packages.

Results

XPO1 expression

Differential expression analysis was performed between tumor tissue and the adjacent normal tissue for each tumor type to investigate the changes in XPO1 expression patterns. Results indicated that XPO1 was significantly overexpressed in most tumor types and significantly underexpressed in a small number of tumors. XPO1 was significantly overexpressed in BLCA, BRCA, CHOL, COAD, ESCA, GBM, HNSC, KIRC, KIRP, LIHC, LUSC, READ, SARC, and STAD and significantly underexpressed in KICH and THCA (Figure 1A). This indicated that XPO1

A

Type Normal Tumor

ns

ns

*

*

ns



ns

ns

XPO1 log2 (TPM+1)CXPO1 log2 (TPM+1)BXPO1 log2 (TPM+1)
57 6826 4828 6 4
Giant cell tumourBloodACC
Upper aerodigestive kidneyHeartBLCA
Multiple myelomaLiverBRCA
LiverMuscleCESCns
ThyroidKidneyCHOL
EsophagusPancreasCOAD
CML Urinary tractStomachDLBC ESCA***
Colorectal BreastSalivary Gland BrainGBM*
Bile ductAdrenal GlandHNSC***
EndometriumColonKICH*** ***
Ovary PancreasEsophagusKIRC KIRP***
Lymphoma DLBCL<not provided>LAML
Lymphoma other MelanomaAdipose TissueLGG
MeningiomaFBlood Vessel ProstateLIHC***
Lung NSC AMLBreastLUAD LUSC*** ***
GliomaSmall IntestineMESO
Lymphoma burkitt StomachLungOV
Ewings sarcomaThyroidPAADns
Lymphoma hodgkinCervix UteriPCPG
OsteosarcomaBladderPRAD
MedulloblastomaSkinREAD
MesotheliomaVaginaSARC
OtherSpleenSKCM
Soft tissue ProstatePituitarySTAD
T-cell ALLNerveTGCT
NeuroblastomaFallopian TubeTHCA
B-cell ALLUterusTHYM-
Leukemia other Lung small cellOvaryUCEC
ChondrosarcomaTestisUCS
NABone MarrowUVM

Figure 1 XPO1 expression in normal tissues, tumor tissues, and cancer cell lines. (A) Differential expression analysis of XPO1 in normal and tumor samples of 33 tumor types (*, P<0.05; *** , P<0.001. The P value of each tumor: BLCA: 5.61e-04; BRCA: 2.97e-09; CESC: 0.08; CHOL: 2.26e-09; COAD: 4.87e-16; ESCA: 1.2e-06; GBM: 0.013; HNSC: 7.85e-15; KICH: 6.58e-09; KIRC: 3.14e-08; KIRP: 2.35e- 05; LIHC: 1.73e-20; LUAD: 2.22e-18; LUSC: 1.71e-25; PAAD: 0.966; PCPG: 0.265; PRAD: 0.852; READ: 0.02; SARC: 0.023; SKCM: 0.883; STAD: 1.27e-15; THCA: 7e-04; THYM: 0.251; UCEC: 0.98). (B) XPO1 expression in normal tissues (based on data from the GTEx database). (C) XPO1 expression in tumor cell lines (based on data from the CCLE database). XPO1, Exportin 1; BLCA, bladder carcinoma; BRCA, infiltrating ductal carcinoma; CHOL, cholangiocarcinoma; COAD, colon adenocarcinoma; ESCA, esophageal carcinoma; GBM, glioblastoma multiforme; HNSC, head and neck squamous cell carcinoma; KICH, kidney chromophobe renal cell carcinoma; KIRC, kidney clear cell renal cell carcinoma; KIRP, kidney renal papillary cell carcinoma; LIHC, liver hepatocellular carcinoma; LUAD, lung adenocarcinoma; LUSC, lung squamous cell carcinoma; PAAD, pancreatic adenocarcinoma; PCPG, pheochromocytoma/paraganglioma; PRAD, prostate adenocarcinoma; READ, rectum adenocarcinoma; SARC, sarcoma; SKCM, skin cutaneous melanoma; STAD, stomach adenocarcinoma; THCA, thyroid carcinoma; THYM, thymic carcinoma; UCEC, uterine corpus endometrial carcinoma.

played different roles in different tumor types and might provide promoting or inhibiting effects during different stages of tumor onset and progression. With selective gene expression, the expression of the same gene in different tissues may not be completely identical, and differences may exist in the biological effects of the gene on various tissues. By utilizing GTEx sample data stored at UCSC Xena, we analyzed the expression of XPO1 in normal tissues. Results indicated that XPO1 expression was relatively higher in the ovary, uterus, bone marrow, testis, and nerve tissues, and relatively lower in the heart and blood tissues (Figure 1B). The analysis of XPO1 expression in tumor cell lines revealed that XPO1 was significantly overexpressed in B-cell acute lymphoblastic leukemia (B-ALL), T-cell ALL, small- cell lung carcinoma and neuroblastoma. This suggested that XPO1 might play a key role in lung cancer, ALL, and neuroblastoma (Figure 1C).

Correlations of XPO1 with clinical characteristics

To investigate the correlations of XPO1 expression with patient prognosis, we performed survival analysis on OS, DSS, DFI, and PFI using the two following methods: the log-rank test and Cox proportional hazards model (Figure 2A-2G, Figure S1A-S1I). When the analysis results of the two methods were consolidated, we observed the following: (I) XPO1 was a risk factor for OS in ACC, LGG, and LIHC, higher XPO1 expression was associated with shorter OS; (II) XPO1 underexpression in ACC, LGG, LIHC, PRAD was associated with longer DSS, but shorter in THYM; (III) XPO1 underexpression in ACC, LIHC, LUAD, and PRAD was associated with longer PFI, and GBM was converse; and (IV) XPO1 underexpression in ACC was associated with longer DFI. Kaplan-Meier Plotter also got similar results (Figure S2A-S2L). To further elucidate the relationships between XPO1 and the various clinical characteristics, the effects of XPO1 on patient age, sex, and clinical stage were investigated (Figure 3A-3I). Results indicated that XPO1 expression was closely related to clinical stage in ACC, BRCA, LIHC, PAAD, SKCM, and THCA. Differences existed in XPO1 expression in BRCA, THCA, and READ among the different age groups, and significant differential expression of XPO1 in LIHC, HNSC, and LUSC also existed between the two sexes. These results suggested that XPO1 expression exerted certain effects on cancer progression, which was in agreement with the observations of XPO1 overexpression

in the majority of tumor types.

Characteristics of molecular-level changes of XPO1 and their correlations with TMB and MSI

We determined the CNV (including amplifications and deletions) frequencies of XPO1 to investigate the diversity of genetic variations of XPO1 among the various tumor types. Results indicated that XPO1 had relatively high CNV frequencies (>5%), with the frequencies of copy number amplifications being generally higher than that of copy number deletions (Figure 4A). When the effects of CNV on XPO1 expression were investigated, we found that XPO1 expression was generally significantly correlated with CNV in tumors, such as BLCA, BRCA, CESC, KIRC, and LICH. Therefore, XPO1 overexpression appeared to be intricately linked to copy number amplification (Figure 4B). Notably, the frequency of copy number deletions of XPO1 in KICH was substantially higher than amplifications, which was consistent with the significant underexpression of XPO1 in KICH mentioned earlier. When the effects of XPO1 on MSI in the various tumor types were investigated, it was found that XPO1 was significantly positively correlated with MSI in ACC, STAD, READ, and CHOL (P<0.05, Spearman’s rank correlation coefficient >0.25) and significantly negatively correlated with MSI in DLBC (P<0.05, Spearman’s rank correlation coefficient 0.25) (Figure 4℃). As many studies have reported an important relationship between TMB and the outcome of immune checkpoint inhibitor therapy, we also performed a correlation analysis of XPO1 and TMB in various tumor types and found that XPO1 expression was significantly positively correlated with TMB in ACC, STAD, READ, LUAD, and LGG (P<0.05, Spearman’s rank correlation coefficient >0.25) (Figure 4D). The results described above further demonstrated that CNV was closely associated with XPO1 overexpression and suggested that XPO1 might affect the prognosis of various cancers through TMB and MSI.

Clinical prognostic value of XPO1 methylation

XPO1 methylation in normal and tumor tissues was measured. The result showed that XPO1 in BLCA, KIRP, LIHC, PRAD and THCA was highly methylated compared with XPO1 in normal tissues (Figure 5A). In particular, survival rate was better with low-methylated

Figure 2 Expression levels and prognostic values of XPO1 in tumor and normal tissues. Survival analysis of XPO1 using the Cox proportional hazards model based on (A) OS, (B) DFI, (C) DSS, and (D) PFI. (E) Kaplan-Meier analysis of the correlations of XPO1 expression in ACC with (from left to right) OS, DFI, DSS, and PFI. (F) Kaplan- Meier analysis of the correlations of XPO1 expression in LGG with OS (left) and DSS (right). (G) Kaplan-Meier analysis of the correlations of XPO1 expression in KIRC with DFI (left) and PFI (right). XPO1, Exportin 1; OS, overall survival; DFI, disease-free interval; DSS, disease-specific survival; PFI, progression-free interval; ACC, adrenocortical carcinoma; KIRC, kidney clear cell renal cell carcinoma.

©

A

B

OS

DFI

C

DSS

D

PFI

9.948(3

Hazard ratio

ACC ALCA

pvalue

Hazard ratio

-001

04916

20.505(1.755-239.623)

ACC

0.001

10.021(3

28763

ACC.

0.001

Hazard ratio

20.186(7.309 59-10

0.793

1.111(0.504-2.449)

A

BRO

9.893

- 19810 684-1.546

1-93818-910-3738

BRCA CESC

1.19910 860-1 19310.869-3-393

9

482 144

BECA

0.124

3.98518-888-2-6153

CESC

0.941

0.8.50

1:3718.740-

21-1.224

CHOL COAD

1.033(0.433-2.463)

4

.876

8 85218 298 1.183

CHOL COAD

0.982

0.79

0.94710.716-1.252 1.9470-110-3609

80

DLBC

0,351

7:368(0,708-2.645)

LẠC

0.68810.418-1-121

0.886

0.801(0.038-16,826)

ESCA GBM

0.628

0.149

9.67110-120 2.905 1 31218 850-2.993

PLAC

1.296

GBM

0.007

1.445(0.920-2 241

12-0.820

5.

19820

ESCA

0.982

0.4990

5.440(1.003-29.493

.495

HNSC

0.991(0.428-2.292)

0.792/0.454-1-284

-29.5

0.486

1.291(0.629-2.647)

1

HINSC

RICH

635 8.873

0.030

0.9590.108-1-301 6.211(1.196-32.25

1.064(0.824-1-15? 3.24210.896-11.734

1.

184

869-3.35

KICH

KIRC KIRE

0.562

1.971(0.199-19.490)

0.113

505410 845 4 846

-

8.299

KIRG

216

LGG

1087 0.532-2.223

810.665-1.899

LGG

901(1.308-2.762 403/1.089-1.80

882

0.001

LGG

1.247 0.890-1.747

0.003

1.10}

A

0.484

0.049

1.495(0.485-4.610)

-8-898

LUAR

0.209 8.209

LUAR

-2 5-1

HVAD LUAD LUSC

0.039

1.3080.002-1.70m

9-485

0.242

MESO

0.739 0,511 0.223 0.00

1:2191 941-2.239)

0.8918-8-2.38 1.4450.840-45

351

1.075(0.704-1.642)

1 90018 888-3.268

‘9421

1.639(0,376-7.148)

SAAD

0.788(0.536-1,157)

8.887

OV

RAD

PAAD PCPG

8.818

19-18319-896-178:818

BAAD SSAB

866-3.112

980 405-32 32

5.971(1.298-27.469)

PSA3

8.681

59239:348-3:438

READ

3.241 0 966-10.87

0.028

0.926

PRAD

1.140(0.071-18 303

READ

0.282 0771

1.54810.698-9 3

REAR

302/0 220-7.709

ERCM

616-2

9.999% 379-1.848

GARC

1 37710 879-2157

STAR SGCT

0.235

0.8/10.694-1.42%

1.377(0.879-2.157)

1.750

&KCM

0.487

1.443(0)

ÈGCT

F

STAD

0.162

112 -08-13.286

0.732(0.407-1.318)

8.491

han 748-1.440

THCA

1-1920 317-17.367

0.797(0.418-1.520

311

3

S

TGCI

0.238

THCA UCEC UČS

0.490

0.10910.588-1-204

0.027

THCA

0.789

ÚČS

0.090

0.141(0.025-0.801

0.86310.294-2439

0.065

2.194(0.850-9.181)

1.490(0.975-2.278)

12/1-245-3.215

UČS

0.005

0.477 0.005

1.539(1.

ŮVM

0.045

1-2

0.492

0.565(0.111-2.883)

UVM

0.048

1.777(1.004-3.145)

UVM

2.106(

5

0.12 0.50 2.0 8.0 32.0

0.062 1e+00 2e+01

0.031 0.500 8e+00 1e+02 Hazard ratio

0.25 1.0 4.0 16.0 Hazard ratio

Hazard ratio

Hazard ratio

E

Cancer: ACC

XPO1 levels+High-Low

Disease-free interval

XPO1 levels-High-Low

Disease-specific survival

XPO1 levels- High- Low

Progression-free interval

XPO1 levels + High-Low

1.00 .

1.00

-

1.00

-

1.00 -

Overall survival

0.75

0.75

0.75

0.75

0.50

0.50

0.50

0.50

4

0.25

P<0.001

0.25

P=0.005

0.25

P<0.001

0.25

P<0.001

0.00

0.00

0.00

0.00

0 1 2 3 4 5 6 7 8 9 10 11 12

0 1 2 3 4 5 6 7 8 9 10 11 12

0 1 2 3 4 5 6 7 8 9 10 11 12

0 1 2 3 4 5 6 7 8 9 10 11 12

XPO1 levels

Times, years

XPO1 levels

Times, years

XPO1 levels

Times, years

XPO1 levels

Times, years

High

-

20

35

23

22 8

6

2

2

2

0

0

High Low

-

19

14

21

9 16

6

6

2

2

2

2

1

2 0

0

High Low

~ -

34

28

8

Low

40

13

23

23

12

39

39

21

18 6

2

2

2

2

0

0

High Low

-

39

31

23

5

3

1

1

0

9

6

5

2

2

9

6

4

3

2

2

13

9

6

5

2

2

2

an

40

28

17

1

7

5

4

2

2

2

T

T

1

T

T

T

1

T

T

1

0

1

2

3

4

5

6

7

8

9 10 11 12

0

1

2

3

4

5

6 7 8

9 10 11 12

0

1

2

3

4

5

6

7

8

9 10 11 12

0

1

2

3

4

5

6

7

8

10 11 12

Times, years

Times, years

F

Times, years

Times, years

Cancer: LGG

Disease-specific survival

Cancer: KIRC

XPO1 levels-High-Low

XPO1 levels+High-Low

XPO1 levels -High-Low

XPO1 levels- High-Low

1.00.

1.00

-

1.00

1.00

-

Overall survival

Disease-free interval

Progression-free interval

0.75

0.75

0.75

0.75

0.50

0.50

0.50

0.50

0.25

P=0.027

0.25

P=0.012

0.25

P=0.018

0.25

P=0.032

0.00

0.00

0.00

0.00

0 1 2 3 4 5 6 7 8 910 11 12 13 14 15 16 17 18 19 20

0 1 2 3 4 5 6 7 8 9 1011 12 13 14 15 16 17 18 1920

0 1 2 3 4 5 6 7 8 9 10 11 12

XPO1 levels

Times, years

0 1 2 3 4 5 6 7 8 9 10 11 12

XPO1 levels

Times, years

XPO1 levels

Times, years

XPO1 levels

Times, years

High LOW

-

202 125 86 86 46 35 28 23 1

8

4

3

2

1

1

1

0

0

9 C

High LOW

7

257 200 124 7 45 66 26 20 13 10 10

258 198 120 81

0

High

1

67 66

GAN

&&

88

80 0

AZ

Ad

11

9

5

Low

2.

I

300

安庆

MN

28

a

Na

5

0

8

7

5

3

3

2

0

0

0

9

5

0

5

0

0

0 1 2 3 4 5 6 7 8 910 11 12 13 14 15 16 17 18 19 20

0 1 2 3 4 5 6 7 8 910 11 12 13 14 15 16 17 18 19 20

0

1

2

3

4

5

6

7

8

9 10 11 12

0

1

2

3

4

5

6

7

8

9 10 11 12

Times, years

Times, years

Times, years

Times, years

Figure 3 Correlations of XPO1 expression with clinical characteristics. Correlations of XPO1 expression in (A) ACC, (B) BRCA, (C) LIHC, (D) PAAD, (E) SKCM, (F) THCA, (G) HNSC, (H) LUSC, and (I) READ with patient age, sex, and clinical stage (*, P<0.05; ** , P<0.01; *** , P<0.001, ns: not statistically significant. The P value of age in each tumor: ACC: 0.623; BRCA: 0.029; LIHC: 0.265; PAAD: 0.961; SKCM: 0.393; THCA: 3.65e-04; HNSC: 0.284; LUSC: 0.217; READ: 0.001. The P value of gender in each tumor: ACC: 0.697; BRCA: 0.286; LIHC: 0.033; PAAD: 0.649; SKCM: 0.739; THCA: 0.952; HNSC: 0.014; LUSC: 0.026; READ: 0.79. The P value of stage in each tumor: ACC: 9.66e-04; BRCA: 0.002; LIHC: 7.71e-04; PAAD: 0.035; SKCM: 0.01; THCA: 0.001; HNSC: 0.399; LUSC: 0.192; READ: 0.906). XPO1, Exportin 1; ACC, adrenocortical carcinoma; BRCA, infiltrating ductal carcinoma; LIHC, liver hepatocellular carcinoma; PAAD, pancreatic adenocarcinoma; SKCM, skin cutaneous melanoma; THCA, thyroid carcinoma; HNSC, head and neck squamous cell carcinoma; LUSC, lung squamous cell carcinoma; READ, rectum adenocarcinoma.

A

ACC ns

B

BRCA ns

C

LIHC

6

ns


Value

XPO1 expression

6

*

**

XPO1 expression

Value

6

ns

*


Adolescence

Adulthood

XPO1 expression

Value

Adolescence

5

Adulthood

Middle age

Middle age

5

Older

5

Adulthood

Middle age

Older

Male

4

Male

Female

4

Stage

4

Older

Male

Female

Stage II

Female

3

Stage I

Stage II

Stage III

3

Stage

Stage III

3

Stage IV

Stage II

2

Stage IV

Stage III

2

Stage IV

Age

Gender

Stage

Age

Gender

Stage

Age

Gender

Stage

D

PAAD ns

E

SKCM

F

THCA

6

ns

*

Value

6

ns

ns

**

Value

6


ns

**

Value

XPO1 expression

Middle age

Adolescence

Adolescence

5

Older

XPO1 expression

Adulthood

XPO1 expression

Male

Female

Middle age

5

Adulthood

4

# Older

Middle age

Older

4

Stage

Stage II

Male

Male

9

Stage III

Female

4

Female

Stage

3

Stage IV

Stage

Stage II

Stage II

2

Stage III

Stage IV

3

Stage III

2

Stage IV

Age

Gender

Stage

Age

Gender

Stage

Age

Gender

Stage

G

HNSC

H

LUSC *

I

READ

6

ns

*

ns

ns

ns

6

**

ns

ns

XPO1 expression

Value

XPO1 expression

6

Value

XPO1 expression

Value

5

Adulthood

Middle age

Middle age

5

Middle age

Older

Older

Older

Male

5

Male

4

E

Male

Female

Female

Female

4

Stage I

Stage

Stage II

Stage II

3

Stage I

Stage II

Stage III

Stage III

3

Stage III

4

Stage IV

Stage IV

2

Stage IV

:

Age

Gender

Stage

Age

Gender

Stage

Age

Gender

Stage

XPO1 than with high-methylated XPO1 in BLCA and UCEC (Figure 5B,5C); the converse was found to be true in CHOL and KIRC (Figure 5D,5E).

Correlations of XPO1 with genomic mutations

The occurrence of malignancies usually involves mutations in multiple genes. The mutation frequencies of XPO1 in the various tumors were generally low (except for a mutation frequency of >5% in UCEC) (Figure 6A). Recently, there was a report in the literature that XPO1 pathogenic mutations could contribute to a poor survival in NSCLC (14). To further elucidate the potential

biological roles of XPO1 in genomic mutations, we analyzed the co-expression of XPO1 and highly mutated genes of the various tumor types. The result suggested that XPO1 expression generally showed significantly positive correlations with the highly mutated genes of the different tumors (Figure 6B-6L, Figure S3A-S3V). This suggested that XPO1 could indirectly promote tumor onset and progression by influencing mutation in other genes.

Potential significance of XPO1 in immune microenvironment changes

The immune microenvironment plays a crucial role in

Percentage, %

A

20

40

60

0

ACC

BLCA

BRCA

CESC

CHOL

COAD

DLBC

ESCA

GBM

HNSC

KICH

KIRC

KIRP

LAML

Amplification

LGG

LIHC

LUAD

LUSC

Deletion

MESO

OV

PAAD

PCPG

PRAD

READ

SARC

SKCM

STAD

TGCT

THCA

THYM

UCEC

UCS

UVM

log2 (XPO1 RSEM)B
911 13
ACCns
BLCA****
BRCA****
CESC****
CHOL*
COAD****Type
DLBC**
ESCA****
GBMnsDeep
HNSC****Deletion
KICHns
KIRC****
KIRP****
LAMLnsShallow
LGG0**
LIHC**Deletion
LUAD****
LUSC****
MESOnsDiploid
OV****
PAAD**
PCPG
PRAD***Gain
ns
READ*
SARC****
SKCM****
STAD
TGCT**** nsAmplification
THCA
THYMns
UCECns
UCS****
UVMns ns
Figure 4 Characteristics of molecular-level changes of XPO1. (A) Somatic CNV frequencies of XPO1 in the 33 tumor types. (B) Correlation of XPO1 CNV type with XPO1 expression (*, P<0.05; ** , P<0.01; *** , P<0.001; **** , P<0.0001; ns, not statistically significant. The P value of each tumor: ACC: 0.83; BLCA: 7.34e-11; BRCA: 2.58e-23; CESC: 2.54e-08; CHOL: 0.043; COAD: 3.7e-05; DLBC: 0.007; ESCA: 2.12e-05; GBM: 0.289; HNSC: 3.66e-13; KICH: 0.081; KIRC: 4.21e-06; KIRP: 3.62e-05; LAML: 0.517; LGG: 0.008; LIHC: 0.002; LUAD: 5.13e-11; LUSC: 5.13e-32; MESO: 0.056; OV: 1.39e-12; PAAD: 0.008; PCPG: 1.77e-04; PRAD: 0.057; READ: 0.012; SARC: 3.66e-05; SKCM: 8.48e-05; STAD: 1.02e-06; TGCT: 0.198; THCA: 0.197; THYM: 0.514; UCEC: 9.26e-11; UCS: 0.18; UVM: 0.919). (C) Correlation of XPO1 expression with TMB (*, P<0.05; *** , P<0.001. The P value of each tumor: ACC: 5.28e-06; BLCA: 3.42e- 05; BRCA: 5.05e-05; CESC: 0.441; CHOL: 0.299; COAD: 0.013; DLBC: 0.413; ESCA: 0.221; GBM: 0.805; HNSC: 1.02e-04; KICH: 0.44; KIRC: 0.911; KIRP: 0.622; LAML: 0.078; LGG: 5.35e-10; LIHC: 0.989; LUAD: 1.58e-16; LUSC: 3.82e-04; MESO: 0.047; OV: 0.01; PAAD: 0.026; PCPG: 0.592; PRAD: 8.87e-05; READ: 0.003; SARC: 0.118; SKCM: 0.004; STAD: 1.48e-08; TGCT: 0.414; THCA: 0.112; THYM: 0.037; UCEC: 0.449; UCS: 0.207; UVM: 0.059). (D) Correlation of XPO1 expression with MSI (*, P<0.05; ** , P<0.01; *** , P<0.001. The P value of each tumor: ACC: 0.034; BLCA: 0.323; BRCA: 0.902; CESC: 0.577; CHOL: 0.01; COAD: 0.077; DLBC: 0.028; ESCA: 0.125; GBM: 0.54; HNSC: 0.565; KICH: 0.652; KIRC: 0.229; KIRP: 0.636; LAML: 0.615; LGG: 0.562; LIHC: 0.521; LUAD: 0.055; LUSC: 1.31e-05; MESO: 0.562; OV: 0.176; PAAD: 0.257; PCPG: 0.249; PRAD: 0.668; READ: 3.66e-06; SARC: 0.297; SKCM: 0.777; STAD: 2.21e-05; TGCT: 0.225; THCA: 0.216; THYM: 0.951; UCEC: 9.09e-05; UCS: 0.966; UVM: 0.529). XPO1, Exportin 1; CNV, copy number variation; ACC, adrenocortical carcinoma; BLCA, bladder carcinoma; BRCA, infiltrating ductal carcinoma; CESC, cervical squamous cell carcinoma and endocervical adenocarcinoma; CHOL, cholangiocarcinoma; COAD, colon adenocarcinoma; DLBC, diffuse large B-cell lymphoma; ESCA, esophageal carcinoma; GBM, glioblastoma multiforme; HNSC, head and neck squamous cell carcinoma; KICH, kidney chromophobe renal cell carcinoma; KIRC, kidney clear cell renal cell carcinoma; KIRP, kidney renal papillary cell carcinoma; LAML, acute myeloid leukemia; LGG, low-grade glioma; LIHC, liver hepatocellular carcinoma; LUAD, lung adenocarcinoma; LUSC, lung squamous cell carcinoma; MESO, mesothelioma; OV, ovarian serous cystadenocarcinoma; PAAD, pancreatic adenocarcinoma; PCPG, pheochromocytoma/paraganglioma; PRAD, prostate adenocarcinoma; READ, rectum adenocarcinoma; SARC, sarcoma; SKCM, skin cutaneous melanoma; STAD, stomach adenocarcinoma; TGCT, testicular germ cell tumor; THCA, thyroid carcinoma; THYM, thymic carcinoma; UCEC, uterine corpus endometrial carcinoma; UCS, uterine carcinosarcoma; UVM, uveal melanoma.

C

BLCA ACC* UVM

D

BRCA

UCS

BLCA *** ACC *** UVM

BRCA ***

UCS

CESC

0.5

UCEC ***

CESC

0.

UCEC

CHOL*

0.2

THYM

CHOL

0.25

THYM*

COAD

THCA

COAD*

THCA

0

0

DLBC*

TGCT

DLBC

TGCT

-0.25

-0.25

ESCA

STAD ***

ESCA

STAD ***

-0.5

-0.5

GBM

SKCM

GBM

SKCM **

HNSC

SARC

HNSC ***

SARC

KICH

READ ***

KICH

READ **

KIRC

PRAD

KIRC

PRAD ***

KIRP

PCPG

KIRP

PCPG

LAML

PAAD

LAML

PAAD*

LGG

OV

LGG ***

OV **

LIHC

LUAD ***

LUAD LUSC ***

MESO

LIHC

LUSC ***

MESO*

Figure 5 Differences and prognostic value of XPO1 methylation. (A) Differences in the negative log (methylation ß-value) of XPO1 in the normal and tumor tissues of the 33 tumor types ( ** , P<0.01; *** , P<0.001. The P value of each tumor: BLCA: 0.001; BRCA: 0.08; CESC: 0.423; CHOL: 1; COAD: 0.623; ESCA: 0.601; GBM: 0.665; HNSC: 0.808; KIRC: 0.237; KIRP: 2.18e-05; LIHC: 3.47e-06; LUAD: 0.062; LUSC: 0.321; PAAD: 0.354; PCPG: 0.275; PRAD: 1.15e-06; READ: 0.836; SKCM: 0.115; THCA: 0.003; THYM: 0.344; UCEC: 0.079). Kaplan-Meier analysis of OS with XPO1 methylation in (B) BLCA, (C) UCEC, (D) CHOL and (E) KIRC. XPO1, Exportin 1; BLCA, bladder carcinoma; BRCA, infiltrating ductal carcinoma; CESC, cervical squamous cell carcinoma and endocervical adenocarcinoma; CHOL, cholangiocarcinoma; COAD, colon adenocarcinoma; ESCA, esophageal carcinoma; GBM, glioblastoma multiforme; HNSC, head and neck squamous cell carcinoma; KIRC, kidney clear cell renal cell carcinoma; KIRP, kidney renal papillary cell carcinoma; LIHC, liver hepatocellular carcinoma; LUAD, lung adenocarcinoma; LUSC, lung squamous cell carcinoma; PAAD, pancreatic adenocarcinoma; PCPG, pheochromocytoma/paraganglioma; PRAD, prostate adenocarcinoma; READ, rectum adenocarcinoma; SARC, sarcoma; SKCM, skin cutaneous melanoma; THCA, thyroid carcinoma; THYM, thymic carcinoma; UCEC, uterine corpus endometrial carcinoma.

A

Type # Normal

Tumor


**


**

6

-log2 (beta value)

1

1

I

A

4

S

2

LUAD

GBM

OV

LUSC

PRAD

UCEC

BLCA

TGCT

ESCA

PAAD

KIRP

LIHC

CESC

SARC

BRCA

THYM

MESO

COAD

STAD

SKCM

CHOL

KIRC

THCA

HNSC

LAML

READ

LGG

DLBC

KICH

UCS

ACC

PCPG

UVM

B

C

1.00

Methy levels - High - Low

1.00

1

Methy levels -High -Low

Overall survival

0.75

Overall survival

0.75

0.50

0.50

0.25

0.25

0.00

P<0.001

0.00

P<0.001

0

1

2

3

4

5

6

7

8

9

10

11

12

13

14

15

0

1

2

3

4

5

6

7

8

9

0 11 12 13 14 15 16 17

18

19 20

Methy levels

Time, years

Methy levels

Time, years

High

205

38 54 35 27

16 9

8

5

4

2

0

0

0

0

0

High

216164111 57 39 25 15 8 4

2

0 000

0 0

0

0

0

0

0

Low

06 155 88

55

43

32

18

13

8

5

4

3

3

3

0

0

Low

7189118 77 53 35

26

8

11

7

4

3

2

2

2

2

1

1 4

1

0

0

T

Y

0 1 2 3 4 5 6 7 8 9 10 11 12 13 14 15

0

1

2

3

4

5

6

7

8

9 10 11 12 13 14 15 16 17 18 19 20

Time, years

Time, years

D

E

1.00

Methy levels High - Low

Overall survival

1.00

Methy levels -High -Low

2

0.75

Overall survival

0.75

0.50

0.50

0.25

P=0.003

0.25

0.00

P=0.003

0.00

0

1

2

3

4

5

0

1

2

3

4

5 6 7 8 9 101

11 12

Methy levels

Time, years

Methy levels

Time, years

High

18

7

Low

18

16

5

11

9

6

4

0

2

0

High Low

59128

09

92

45

26

20

17

160121 86

80

62

12

3

1

T

T

T

T

T

T

64

48

30

21

13

6

5

1

0

0

T

T

r

T

T

T

T

T

T

T

T

T

T

0

1

2

3

4

5

0

1 2 3 4 5 6 7 8 9 10 11 12

Time, years

Time, years

Percentage, %

Percentage, %

G

Percentage, %

D

Percentage, %

J

4

5

6

25

50

75

10

10

15

20

0

1

2

3

0

5

0

5

ACC

0

.

PBRM1

APC

DNMŢ3A

ARID 1A

BLCA

BRCA

TP53

FLTS

BAP1

TIN

NPM

RUNX1

EPHA2

CESC

KRAS

IDH1

CHOL

TP53

MUC16

COAD CUAD

SYNE1

DLBC

FAT4

CHDI MUCSB

MAP1B

ESCA GBM

MUC 16

FBXW

MUC16

LAPLP

ELF3

FOR2

HNSC

LAP1B

NRAS

TP53

KMT2D

READ

LAML LAML

CHOL

KICH

IDH1

KIRC KIRP

SMAD4

KRAS

NEB

CSMD1 PIK3CA

CMYA5

DNAH5

PCLO

LAML LIGG LGG

ALB

FAT3 HVA1

CEBER

APOB

LIHC

LUAD

MACE

AHINAK

DNAH11

MACF

LUSC

OB SON

SME

FGER

UBRA

BIRRA

MESO

ASXL

BOOK

OV

ISNEB

USHOA

BOORL

LAMA3

PAAD

PCPG

DDAD

COL6A3

ANK2

MACF1

SYNE

DNAH17 KIF19

PRAD

ARCA13

DCAFAL2

READ

SARC

SLITRK5

PRUNE2

AHMAN

DNAKS

SKCM

CEMDE CSMDS

UNC13C ZNF804B

GRILLA GRIK

OLDU98

ADAM30

STAD

LRP1B

TGCT

Cor

P value

Cor

.

P value

THCA

A

.

·

Cor

THYM

A

·

P

0.0

0.2

0.4

0.6

<0.0001

<0.001

<0.01

<0.05

>0.05

value

0.0

0.2

0.4

<0.0001

<0.001

<0.01

<0.05

>0.05

-0.5

0.0

0.5

<0.0001

<0.001

<0.01

<0.05

>0.05

UCEC

UCS

UVM

B

Percentage, %

K

Percentage, %

H

Percentage, %

E

Percentage,

%

10

15

10

20

30

20

40

60

10

20

30

40

50

0

0

0

0

5

APC

TP53

KIT

BAP1

TP53

KMT2D

KRAS MUC4

NEZ

TP53

TIN KA IN

TTN

KOMOA

NRAS

SETD2

MUC16

SYNET

ARID1A

PIK3CA

SRCAP

LAIPT

PIK3CA

MUC5B

FAT4

FAT4

SYRE

BIRC6 PCLŐ

PTCH1

CCDC168 LAMAS

DESON

RYR2

KMIZE

45836

LRP18

NCOR1 PARM

DNAH5

EP300

BLCA

NISCH

PBRMI

PCLO

COAD COAD

COAD

MACF1

TRIP 12

TGCT TGCT TGCT

MESO MESO

CSMUS LAP18

ELG

NOTCH3

DST ARID2

BATA

KNIC

ZNF469

ABCA13

DNAH11

DNEAT3

FOXPA

OGDHL RANGA BAZ2B

USH2A USHZA

CSMUS

DMD

ELIS ATM

ATADE

CSMDI

LENERI HECTD4

DNHD1

ALPK3 NDSTO

HYHS RYR1

CBN

EMID1 PIK3CA SACS

FBXW

CREBBP

HTR7

H

LAP2

NEB

KMT2D KMVER

ZEUXA

ANKRD50

FLG

NLRP7

DNAHS

NEB

SVINE

EML5

CCDC168

SY NE

NLMP9

MUC4

ADSONE

AHLANG

HMCN1

BRAF

OBSUN

MUC17

DOPO

MROH2B

FLG

ANKRD30A

Cor

·

Cor

Cor

.

·

P

-0.50

-0.25

0.00

0.25

0.50

0.75

<0.0001

<0.001

<0.01

<0.05

>0.05

value

-0.2

0.0

0.2

0.4

<0.0001

<0.001

<0.01

<0.05

>0.05

P value

0.0

0.2

0.4

<0.0001

<0.001

<0.01

<0.05

>0.05

P value

0.0

0.2

0.4

Cor

<0.0001

<0.001

<0.01

<0.05

. >0.05

P value

Percentage, %

Percentage,

di

F

Percentage,

de

C

Percentage, % L

20

30

Zhao et al. Pan-cancer analysis of XPO1

I

10

0

20

40

60

8

12

10

20

30

4

0

0

0

TP53

PTEN

TTN

PIK3CA KMI2C

PTEN

SPOP

15291

PIK3CA

MUC16

FOXA1

EGFR-

MUCHO

MUSS

ARIDIA

KMT2D

TP53

AMOR

MUCHO

DMD ELG

MUC16

SPA1

NF1-

RYR2

PIK351

SPIA

SPTA1

EP300

KMT2D KMUSE

LAP1B

RB1

FBXW7

CSMD3

AIM

ATRX

CSMD3

PIKORA

PORRET

MILES

MUCIL

CTNMBS

GBM GBM

CESC

HYR2

PTEN

LRP1B

HYR2

SYNE1 MUC5B

PRAD PRAD

USH2A ADGRV1

PREBA LRP2

FAT4 ZEMX4 OBSČÍN DCLO POER

UCEC UCEC UCEC

PRAD

OBSCN

HMCIH

CSMD1

KMT2B

CACINATE

KDMBA

APOB. FLG2.

SYNE PCLO

RYB1 FAT3

COL6A3-

AP

DNAH5-

DST

NEP

KMCO-

MUC5B

MACF1

ZMYMS

OBSCN

ELG

MACE

AHNAN

DNADE

NEB

USH2A

O

DNAHZ LRP1B

HMC

DNAH3

PRKDC

DNAHE

AHNAK2

“MON1

CHD4

DNAH5 FAT3

CDKY PCLO

DNAHB-

USH2A-

DNAH2

COL11A1

MUC17-

LRP2

Cor

P value

Cor

. >0.05

P value

0.0

0.2

3

Cor

· >0.05

P value

CCDC168

0.0

0.2

0.4

.4

<0.0001

<0.001

<0.01

<0.05

-0.2

0.0

0.2

0.4

0.6

Cor

<0.0001

<0.001

<0.01

<0.05

.>0.05

P value

0.0

0.2

0.4

0.6

<0.0001

<0.001

<0.01

<0.05

>0.05

-0.2

<0.0001

<0.001

<0.01

<0.05

Figure 6 Genetic mutations of XPO1. (A) Mutation frequencies of XPO1 in the 33 tumor types. Correlations of XPO1 expression with expression levels of the top 30 highly mutated genes in (B) BLCA, (C) CESC, (D) CHOL, (E) COAD, (F) GBM, (G) LAML, (H) MESO, (I) PRAD, (J) READ, (K) TGCT, and (L) UCEC. Circle size indicates the magnitude of the P value and shade indicates the magnitude of the Spearman’s rank correlation coefficient. XPO1, Exportin 1; BLCA, bladder carcinoma; CESC, cervical squamous cell carcinoma and endocervical adenocarcinoma; CHOL, cholangiocarcinoma; COAD, colon adenocarcinoma; GBM, glioblastoma multiforme; LAML, acute myeloid leukemia; MESO, mesothelioma; PRAD, prostate adenocarcinoma; READ, rectum adenocarcinoma; TGCT, testicular germ cell

tumor onset and progression as well as patient prognosis. Therefore, correlation analysis was performed on XPO1 expression and the stromal and immune scores of the various tumor types were calculated using the ESTIMATE algorithm. We found that XPO1 expression exhibited tumor; UCEC, uterine corpus endometrial carcinoma.

negative correlations with both the stromal and immune scores. In particular, XPO1 was significantly negatively correlated with both the stromal and immune scores of ACC, GBM, LUSC, SARC, and STAD (P<0.05, R 0.25) (Figure 74-7E), significantly negatively correlated with

Figure 7 Effects of XPO1 on the tumor immune microenvironment. Correlations of XPO1 expression with ESTIMATE-calculated immune score (left) and stromal score (right) in (A) ACC, (B) GBM, (C) LUSC, (D) SARC, and (E) STAD. (F) Correlations of XPO1 expression with the CIBERSORT-calculated contents of 22 immune cell types in the various tumor types. XPO1, Exportin 1; ACC, adrenocortical carcinoma; GBM, glioblastoma multiforme; LUSC, lung squamous cell carcinoma; SARC, sarcoma; STAD, stomach adenocarcinoma.

A

Cancer: ACC

Cancer: ACC

B

Cancer: GBM

Cancer: GBM

R =- 0.39, P=0.00041

R =- 0.41, P=0.00017

5.0

‘R =- 0.41, P=3.4e-08

5.0

R =- 0.42, P=2.5e-08

:

%

4

4

4.5

4.5

XPO1

XPO1

XPO1

XPO1

3

3

4.0

4.0

3.5

3.5

2

2

-1000

0

1000

2000

-1000

0

1000

-1000

0

1000

2000

-1500-1000-500

0

500

1000 1500

Immune score

Stromal score

Immune score

Stromal score

C

Cancer: LUSC

Cancer: LUSC

D

Cancer: SARC

Cancer: SARC

5.5

6

R =- 0.31

P=2:1e-12

5.5

6

R =- 0.38

P<2.2e-

$6

R =- 0.48, P<2.2e-16

R =- 0.55, P<2.2e-16

5.0

5.0

4.5

4.5

XPO1

5

XPO1

5

XPO1

4.0

XPO1

4.0

4

4

3.5

3.5

3.0

3.0

2.5

2.5

-1000

0

1000

2000

3000

-2000

-1000

0

1000

2000

-1000

0

1000 2000 3000

-1000

0

1000

2000

Immune score

Stromal score

Immune score

Stromal score

E

Cancer: STAD

Cancer: STAD

F

Neutrophils Eosinophils

Mast cells activated

Mast cells resting

Dendritic cells activated

R =- 0.27, P=2e-07

R =- 0.37, P=1.7e-13

Dendritic cells resting

P value

5

5

Macrophages M2

<0.05

Macrophages M1

<0.01

Macrophages MO

<0.001

Monocytes

<0.0001

XPO1

NK cells activated

4

XPO1

4

NK cells resting

Cor

T cells gamma delta

T cells regulatory (Tregs)

0.6

T cells follicular helper

0.3

0.0

3

3

T cells CD4 memory activated

T cells CD4 memory resting

-0.3

T cells CD4 naive

-0.6

T cells CD8

Plasma cells

B cells memory

-1000

0

1000

2000

3000

-2000

-1000

0

1000

2000

B cells naive

Immune score

Stromal score

ACC BICA

BRCA

CES CHOL

COAD

DLBO

ESCA

GBM

HNCC

HNSC

RP

LAML

LGG

MESO

PAAD

PCPG

PRAD

READ

SARC

KCM

STAR

THCA

THYM

UCEC

UVM

immune score in CESC, ESCA, KIRP, LAML, PCPG, UCS, and MESO (P<0.05, R 0.25), and significantly negatively correlated with stromal score in OV and TGCT (P<0.05, R 0.25) (Figure S4A-S4R). The result obtained from the CIBERSORT algorithm showed that XPO1 was generally negatively correlated with the various immune cell contents (except for M1 macrophages, activated memory Th cells and resting memory Th cells) (Figure 7F). Therefore, XPO1 could also promote tumor onset and progression by influencing the tumor immune microenvironment.

Interactions of XPO1 with other genes and XPO1 molecular functions

To further investigate the molecular mechanisms by which XPO1 affected the tumor microenvironment, we performed co-expression analyses of XPO1 with immune checkpoint genes and cancer driver genes. XPO1 generally showed significantly positive correlations with the expression of immune co-inhibitory receptors, such as ADOPA2A, BTLA, CD160, CD200, CD200R1, PDCD1LG2, and

Figure 8 Co-expression analyses of XPO1 and specific genes. (A) Co-expression analysis of XPO1 and immune checkpoint genes. (B) Differential expression of the top five driver genes in each tumor type with the most significant differences, which were determined from the grouping of genes based on the median XPO1 expression level after the elimination of normal samples. (C) Co-expression analysis of XPO1 and driver genes with the most significant differences. (D) Co-expression analysis of XPO1 and the top five most-correlated biological pathway-related genes calculated based on GSEA results. XPO1, Exportin 1; GSEA, gene set enrichment analysis.

A

B

ZBTB16

VTCN1

VSIR

TNFSF9

UGT

TNFSF4

TNFSF18-

TNFSF15-

TNFSF14

TNERSF9.

SA

TNFRSF8.

TNFRSF4-

PRI

TNFRSF25-

INFRSF18

NY

TNFRSF14

TMIGD2

TIGIT

MY

PDCD1LG2

PDCD1 NRP1

LGALS9

LAIR1

Cor

Log FC

LAG3

KIR3DL1

5.0

IDO2

0.6

M

IDO1

ICOSLG

cos

0.3

2.5

HHLA2

0.0

HAVCR2

CTLA4 CD86

0.0

FG

CD80.

-0.3

ES

-2.5

CD70-

EBE

-5.0

CD48

CD44

CD40LG

P value

CD40

<0.05

P value

CD28.

CD276

DCS

CD274- CD27.

<0.01

· < 0.05

CD244.

<0.01

CD200R1

<0.001

SOL

· < 0.001

CD200-

CD160.

<0.0001

<0.0001

BTNL2

BTLA

ADORA2A

C

D

HO)

CD

SP

PE

NK

CY

P value

P value

NA

<0.05

· <0.01

<0.05

<0.001

<0.01

<0.0001

NES

UG

Cor

3

0.50

2

1

0.25

0

E

马V

0.0

HOX

-0.25

DOSTA

-0.50

EP

w

HOXC13

CTLA4, and negative correlations with immune co- stimulatory receptors, such as TNFRSF14, TNFRSF18, TNFRSF4, and TMIGD2 (Figure 8A). Mutations in cancer driver genes favor the promotion of tumor onset and progression. To further investigate the effects of XPO1 on gene mutations, co-expression analysis was performed with XPO1 and driver genes with high differential expression. XPO1 expression was highly positively correlated with driver gene expression, which indicated that XPO1 may serve as a potential driving factor of tumor onset and

progression (Figure 8B,8C). GSEA revealed that cell cycle- targeting genes encoding E2F transcription factors, G2/M checkpoint genes, and genes associated with the assembly of the mitotic spindle apparatus were downregulated in the XPO1 overexpression group. Genes related to coagulation system components, genes encoding complement system components, genes related to oxidative phosphorylation, genes encoding proteins involved in the processing of drugs and other xenobiotics, and genes that upregulate adipocyte differentiation were upregulated in the XPO1

underexpression group (Figure 8D). Therefore, XPO1 might affect the tumor immune microenvironment by regulating the expression of immune checkpoint genes and served as a driving factor for the promotion of mutations in cancer driver genes, thereby promoting tumor onset. The effects of XPO1 on the tumor microenvironment might also be exerted through influences on biological processes, such as the cell cycle and oxidative phosphorylation.

Discussion

The inhibition of XPO1 expression can serve as a potential treatment strategy for a wide variety of tumors, such as malignant tumors of the bladder, FLT3 mutation-induced acute myeloid leukemia, melanoma, stomach cancer, cervical cancer, ovarian cancer, pancreatic ductal adenocarcinoma, glioma, and osteosarcoma (15-17). In this study, we performed a systematic description of XPO1 expression across multiple cancer types by analyzing the transcriptome expression data of 33 types of tumors from the UCSC Xena database. Our results indicated that XPO1 was significantly overexpressed in BLCA, BRCA, CHOL, COAD, ESCA, GBM, HNSC, KIRC, KIRP, LIHC, LUSC, READ, SARC, and STAD. To further determined if XPO1 was generally overexpressed in tumors, we described XPO1 expression by utilizing normal tissue transcriptome data from GTEx and tumor cell line transcriptome data from CCLE. The mean expression of XPO1 in the various tumor cell lines was higher than that of normal tissues. XPO1 overexpression is a key characteristic of lung cancer, osteosarcoma, glioma, pancreatic ductal adenocarcinoma, cervical cancer, ovarian cancer, renal cell carcinoma, esophageal cancer, stomach cancer, hepatocellular carcinoma, acute myeloid/ lymphocytic leukemia, multiple myeloma, and colon cancer. XPO1 plays a crucial role in tumor progression by influencing p53 phosphorylation or survivin protein expression (17-29). Our results also indicated that XPO1 overexpression was an important characteristic of many tumor types and might influence tumor progression.

TMB, which refers to the number of gene mutations present in tumor cells, can be utilized as a biomarker of certain tumor types and predicts the effects of immunotherapy. TMB has been used as a novel biomarker for the prediction of the clinical benefits of nivolumab combined with ipilimumab in the treatment of non-small cell lung cancer (30). MSI is present in various cancers, such as colon, endometrial, cervical, esophageal, skin, and breast cancers (31). Patients with colon cancer with characteristics

of MSI have a better prognosis compared with those without MSI, and differences exist in the response to chemotherapy between the two groups (32). Our results indicated that XPO1 expression was significantly correlated with the presence of TMB and MSI in many tumor types, such as ACC and STAD. Therefore, we deduced that the molecular mechanisms of the effects of XPO1 on tumors might be related to its role in nuclear protein transport. By affecting or altering the transport of certain proteins, XPO1 might exert effects on biological processes, such as the cell cycle, DNA replication, and transcription, thereby indirectly inducing mutations and changes in expression in certain genes.

The results of GSEA indicated that XPO1 expression affected genes related to the G2/M checkpoints and oxidative phosphorylation, causing disturbances to related signaling pathways or biological processes. XPO1 expression also showed significantly positive correlations with the expression of highly mutated genes and cancer driver genes, suggesting that XPO1 could play a role in the early stages of tumor onset. Therefore, the early use of XPO1 inhibitors might provide better prognostic effects.

During the tumor onset and development process, tumor progression is determined by the continuous interactions between the tumor and host immune response (33). In other words, the progression and survival outcome of a tumor is largely dictated by its immune microenvironment. To elucidate the relationships of XPO1 with host immunity, we utilized the ESTIMATE and CIBERSORT algorithms to evaluate immunity-related characteristics and found that XPO1 expression was generally negatively correlated with immune and stromal scores, negatively correlated with the contents of regulatory T cells, CD8+ T cells, and plasma cells, and positively correlated with M1 macrophages, Tfh cells, and activated and resting CD4+ T cells. Correlation analysis of the expression of XPO1 and immune checkpoint genes revealed that XPO1 was generally positively correlated with immune co-inhibitory receptors and negatively correlated with immune co-stimulatory receptors. This indicated that XPO1 overexpression could regulate the tumor immune microenvironment and inhibited the host immune response, ultimately causing tumor immune evasion and progression.

Conclusions

We utilized pan-cancer data for the multi-dimensional analysis of the expression and molecular mechanisms of

XPO1 in clinical characteristics and genomics. We also systematically elucidated the biological roles of XPO1 in various cancers. The results of this study provided a theoretical basis for clinical applications of XPO1 inhibitors.

Acknowledgments

Thank all the datasets’ owners who made the valuable data public.

Funding: None.

Footnote

Reporting Checklist: The authors have completed the REMARK reporting checklist. Available at https://dx.doi. org/10.21037/tcr-21-1646

Conflicts of Interest: All authors have completed the ICMJE uniform disclosure form (available at https://dx.doi. org/10.21037/tcr-21-1646). The authors have no conflicts of interest to declare.

Ethical Statement: The authors are accountable for all aspects of the work in ensuring that questions related to the accuracy or integrity of any part of the work are appropriately investigated and resolved. All procedures performed in this study involving human participants were in accordance with the Declaration of Helsinki (as revised in 2013).

Open Access Statement: This is an Open Access article distributed in accordance with the Creative Commons Attribution-NonCommercial-NoDerivs 4.0 International License (CC BY-NC-ND 4.0), which permits the non- commercial replication and distribution of the article with the strict proviso that no changes or edits are made and the original work is properly cited (including links to both the formal publication through the relevant DOI and the license). See: https://creativecommons.org/licenses/by-nc-nd/4.0/.

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